Validación del instrumento de medida haemophilia activities list para la evaluación de las capacidades autopercibidas de actividad física en pacientes con hemofilia

Abstract

Introduction: Hemophilia is a congenital disease characterized by musculoskeletal hemorrhages and physical sequelae from early ages. Objectives: To identify and analyze the psychometric characteristics of the instruments used in the evaluation of physical activity in patients with hemophilia. To validate the Spanish version of the Haemophilia Activities List (HAL) questionnaire. Methods: 132 adult patients with hemophilia were recruited (mean age: 36.95±7.69; mean joint damage: 56.84±16.61 points). They were administered the HAL questionnaire, consisting of 42 items, grouped into seven dimensions (Lying down, sitting, kneeling and Standing; Functions of the legs; Functions of the arms; Use of transportation; Self care; Household tasks; and Leisure activities and Sport). Results: A high internal consistency of the total scores in the questionnaire (ɑ > 0.97) and of the seven dimensions that compose it (ɑ > 0.80) was found. Too a high stability of the questionnaire scores (r > 0.97) was found. Conclusions: The Haemo-QoL, Functional Independence Score in Hemophilia, Haemophilia & Exercise Project Test Questionnaire and Haemophilia Activities List are the most used instruments to measure physical activity related to quality of life and the impact of self-perceived functional abilities in these patients. The Spanish version of the HAL questionnaire presents optimal results in the analysis of the homogeneity and reliability index, reproducibility and structural validity. The Spanish version of this questionnaire produce reliable scores for use in adult patients with hemophilia.